Pesquisa sobre: SUCCINATE-SEMIALDEHYDE DEHYDROGENASE 
Descritores Encontrados: 1
Mostrando: 1 .. 1  

 1 / 1 DeCS     
Descritor Inglês:   Succinate-Semialdehyde Dehydrogenase 
Descritor Espanhol:   Succionato-Semialdehído Deshidrogenasa 
Descritor Português:   Succinato-Semialdeído Desidrogenase 
Sinônimos Inglês:   Dehydrogenase, Succinate Semialdehyde
Dehydrogenase, Succinate-Semialdehyde
Dehydrogenase, Succinic Semialdehyde
NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase
Semialdehyde Dehydrogenase, Succinate
Semialdehyde Dehydrogenase, Succinic
Succinate Semialdehyde Dehydrogenase
Succinic Semialdehyde Dehydrogenase  
Categoria:   D08.811.682.657.163.843
Definição Inglês:   An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA). 
Nota Histórica Inglês:   2006(1980); use ALDEHYDE OXIDREDUCTASES 1977-1979 
Qualificadores Permitidos Inglês:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DF deficiency DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Número do Registro:   50619 
Identificador Único:   D050644 

Ocorrência na BVS:
 

Similar:

 
DeCS