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DeCS
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Descritor Inglês:
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Succinate-Semialdehyde Dehydrogenase
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Descritor Espanhol:
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Succionato-Semialdehído Deshidrogenasa
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Descritor Português:
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Succinato-Semialdeído Desidrogenase
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Sinônimos Inglês:
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Dehydrogenase, Succinate Semialdehyde
Dehydrogenase, Succinate-Semialdehyde
Dehydrogenase, Succinic Semialdehyde
NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase
Semialdehyde Dehydrogenase, Succinate
Semialdehyde Dehydrogenase, Succinic
Succinate Semialdehyde Dehydrogenase
Succinic Semialdehyde Dehydrogenase
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Categoria:
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D08.811.682.657.163.843
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Definição Inglês:
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An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA). |
Nota Histórica Inglês:
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2006(1980); use ALDEHYDE OXIDREDUCTASES 1977-1979
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Qualificadores Permitidos Inglês:
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Número do Registro:
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50619
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Identificador Único:
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D050644
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Ocorrência na BVS:
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Similar:
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DeCS
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